Abstract
Background. Malignant fibrous histiocytoma (MFH) is the most common soft tissue sarcoma in adults, usually arising in the extremities or trunk, however primary MFH of the lung is rare. Case. A 65-year-old woman was admitted because of an abnormal shadow on chest X-ray film. Chest CT scan showed an ill-defined solid mass shadow in the left S6 region. We performed partial resection of the left lower lobe, as the frozen section diagnosis was sarcomatous tumor, suggesting pulmonary metastasis from soft tissue sarcoma. Tumor cells were positive for CD68, but we could not detect any primary lesions. Therefore, the final diagnosis was primary MFH of the lung. Conclusion. Previous clinical reports suggest a poor prognosis of primary MFH of the lung because of the high incidence of local recurrence or distant metastasis after surgery. To prevent recurrence after surgery, pulmonary lobectomy was recommended as a curative procedure in several reports in the literature. In this case, partial resection was performed without additional lobectomy and postoperative adjuvant therapy. However, the patient has been doing well with no evidence of local recurrence or distant metastasis for 3 years postoperatively.
