Abstract
Alport's syndrome and benign familial hematuria are typical conditions of familial hematuria. The former is a disease with poor prognosis. It complicates with neurological hearing impairment and develops into terminal renal failure. The latter continues to produce hematuria for a long time, however, clinical situation is benign. It is very important to distinguish both diseases early. We investigated electronmicroscopically renal biopsy specimens from members of families with familial hematuria. We concluded that electronmicroscopic examination is useful to distinguish between Alport's syndrome and benign hematuria.
