An alveolar soft part sarcoma without recurrence for 21 years after resection of metastases

Abstract

Alveolar soft part sarcoma (ASPS) is a rare soft tissue tumor, typically affecting young patients. Although it shows a relatively indolent clinical course without metastases, the ultimate prognosis in patients with metastases is poor. This report presents a female patient with pulmonary metastases who survived without recurrence following pulmonary metastasectomies for 21 years. She underwent surgery to remove a mass in her abdominal wall at 12 years old. The pathologic diagnosis was ASPS. She was referred to our department to undergo surgery for metastases occurring in both lungs 2 years later. She underwent surgery twice to remove the metastases. The pathologic diagnosis was metastatic ASPS. She has remained recurrence-free for 21 years since the metastasectomies.