Extralobar pulmonary sequestration presenting as a superior mediastinal tumor

Abstract

An 18-year-old woman was admitted to our hospital with an abnormal shadow in the superior mediastinum on a chest radiograph. Chest CT and MRI revealed a mass with cyctic and solid components on the right side of the superior mediastinum. Thoracoscopic surgery was performed to remove the mass, diagnosed as a superior mediastinal tumor. The mass existed in the superior mediastinum with a tiny stalk on the cranial side. The resected mass was composed of multiple cysts covered with ciliated columnar epithelium, cartilage, smooth muscle, bronchial glands, and collapsed alveoli. Arteries increased in the specimen, which consisted of thick three-layered walls, but venous drainage was not apparent. The mass was covered with pleura, and pathologically diagnosed as extralobar pulmonary sequestration.