1993 Volume 7 Issue 6 Pages 717-721
A 36-year-old female was admitted because of recurrent spontaneous pneumothorax after tube drainage. Neither chest X-ray nor chest CT scan showed any abnormal findings. Surgical operation combined with pleurodesis revealed the presence of multiple bullae and granular nodules were incidentally found in the lung. A biopsy specimen revealed typical pulmonary lymphangiomyomatosis. She has had no episode of pneumothorax and has been asymptomatic since the thoracotomy one year ago. This patient had early stage pulmonary lymphangiomyomatosis. Even if no symptoms are present and X-rays are negative, in cases of repeated pneumothorax in females, histological studies need to be performed for diagnostic confirmation.