Esophageal duplication is a rare congenital anomaly that occurs anywhere along the alimentary tract from the mouth, down to the anus and the nearby organs. We report herein on a patient with esophageal duplication accompanied with stridor, in whom an imaging study was useful. A 4-month-old boy was referred to our hospital with stridor, for which medical treatment had not shown any effect. We performed laryngeal endoscopy and ultrasonography, and computed tomography (CT). Laryngeal endoscopy showed the larynx biased to the right. Ultrasonography indicated the muscular rim sign. CT displayed a tumor (3×3×2cm) near the esophagus, and the trachea was displaced by the mass. Surgical excision of the tumor was perfomed, because esophageal duplication was suspected based on the examinations. The pathological diagnosis showed esophageal duplication. When a case of stridor is not cured by medical treatment, neoplastic lesion should be considered, and it is necessary to perform an imaging study.
