Abstract
A 3-year 8-month-old girl visited our clinic complaining of a feeling of fullness in the right ear. She had passed the newborn hearing screening (NHS) with the automated auditory brainstem response (automated ABR) test. CT imaging of the right temporal bone revealed internal auditory canal stenosis. MRI showed that the right cochlear nerve was thin, but continuous. No ABR was evoked even by 90 dB nHL of click stimuli to the right ear. Distortion product otoacoustic emission (DPOAE) response from the right ear was not clear. These results indicate that hearing impairment might appear after birth in patients with congenital unilateral internal auditory canal stenosis.
