A new classification system for labyrinthine anomalies is introduced.
This system takes into consideration the varying degrees of pathology of the labyrinth which have been described in the literature and also includes anomalies which have not been categorized previously.
With this classification system, anomalies of the labyrinth can be classified into two major categories: aplasia and hypoplasia. The hypoplasia category is further divided into three types: combined, bony, and membranous. These three subtypes are further divided into 16 different groups: nine groups in the combined type, three in the bony type, and four in the membranous type, depending on which structures of the labyrinth are involved in the hypoplasia.