Abstract
Congenital nystagmus is usually noted at birth or during childhood and is present throughout life. Congenital nystagmus in itself is not a disease which causes dizziness.
However, when it is present coincidentally with certain other diseases, it may give rise to dizziness which cause difficulty in diagnosis.
We examined 14 patients with congenital nystagmus who complained of dizziness. Eight patients had orthostatic dysregulation and four had peripheral vestibular dysfunction which was associated with canal paresis and/or sensorineural hearing loss.
More studies are needed to clarify the mechanism of dizziness in patients with congenital nystagmus.