A 56-year-old woman visited our hospital because of nasal pain. Physical examination revealed a gray mass in the right nasal cavity. Precontrast CT scan showed a lesion with iso-density relative to the muscles, which had intermediate signal intensity on Ti-weighted MR image and high, partially low, signal intensity on T2-weighted image. The mass was totally removed by an endonasal approach, and histological examination showed interlacing bundles of tumor cells, confirmed as smooth muscle cells by immunohistochemistry and electron microscopy.