The case of an 13-month-old boy with Langerhans cell histiocytosis of the bilateral temporal bone is presented. He was referred to our clinic after three months of conservative treatment following a diagnosis of chronic otitis media, and the development of a polyp. A histopathological examination and computerized tomography were performed, which were essential for the diagnosis. Chemotherapy consisting of VCR, AraC and prednisolone was initiated, with a good response so far. Satisfactory bone repair has proceeded spontaneously over the six-month follow-up period. In cases of aural polyp, especially when those demonstrating resistance to conservative therapy, early evaluation using sufficient biopsy tissue and computerized tomography should be considered.