Hepatic Left Lateral Segmentectomy with Fenestration for Symptomatic Polycystic Liver Disease

Abstract

There are several treatment options for symptomatic polycystic liver disease, but no consensus has been established on the best surgical practice for this disease. The patient was a 49-year-old Japanese woman with autosomal dominant polycystic kidney disease. Her chief complaint was massive abdominal distention and early satiety. CT showed a polycystic kidney and liver, and the stomach was compressed by the massive polycystic liver. Liver and renal functions were within normal levels. The left lateral segment of the liver was almost replaced with large cysts and the posterior segment was occupied by several cysts. Hepatic left lateral segmentectomy and fenestration in the posterior segment were performed. After the surgery, her chief complaint improved, and the volume of the parenchyma increased by 20%, while that of the liver decreased to 54%.