Lipoma is a common benign tumor of the soft tissue. It predominantly occurs in subcutaneous regions, but can also be found in intramuscular, retroperitoneal, and intraosseous locations. According to the literature, the incidence of intraosseous lipoma is less than 0.1% of all bone tumors. Intraosseous lipoma generally occurs in the metaphysis of long bones and the calcaneus, and is rarely seen in the jawbone. To our knowledge, only 25 cases of intraosseous lipoma of the jawbone were reported from 1948 to 2014. There have been no documented cases of intraosseous lipoma arising in the mandibular condyle. In this paper, we reported a rare case of intraosseous lipoma arising in the right mandibular condyle and causing marked mandibular deviation in an 86-year-old woman.