Juvenile ossifying fibroma (JOF) is a rare disease that develops before 15 years of age and grows relatively rapidly. JOF is classified into juvenile trabecular ossifying fibroma (JTOF) and juvenile psammomatoid ossifying fibroma (JPOF) according to the pathological variants. We report an extremely rare case of JOF with conglomeration of trabecular and psammomatoid variants in the maxilla. The patient was an 11-year-old boy who presented to our hospital with prolonged retention of the right maxillary first deciduous molar. Intraoral examination at presentation showed prolonged retention of the right maxillary first and second deciduous molars, buccal dislocation of the right maxillary first premolar, and buccolingual swelling of the right maxillary bone in the molar region. Radiological examination showed a well-circumscribed radiolucent quail-egg-size lesion, extending from the right maxillary first premolar to the apex of the first molar. The right maxillary first premolar had rotated, and the second premolar was impacted in the upper distal portion of the lesion. A biopsy was performed, and JOF was diagnosed. Tumor enucleation and curettage were performed with the patient under general anesthesia. No recurrence occurred during the 6-year follow-up period.