1986 Volume 32 Issue 12 Pages 2301-2310
Two cases with basal cell nevus syndrome and a review of literature are presented. Multiple jaw cysts, hypertelorism, palmer and planter pits, and a calcification of falx cerebri and of tentorium were observed in both cases.
Beside this syndrome, a 22-year-old female (case 1) had a cleft lip-alveolus, and another 31-year-old woman (case 2) had a basal cell epithelioma in the occipital skin and bridging of sella turcica radiographically.
Frequency of the cleft lip, alveolus, and/or palate with this syndome, including one casc of ours, was 12.8% and the incidence was far more frequent compared with the national avarage.
Considering a high recurrence of odontogenic keratocysts, it was suggested that a sufficient curattage of the bony walls after the removal of cysts might be useful for the treatment of odontogenic keratocysts.
