Alveolar soft-part sarcoma is a rare malignant neoplasm of uncertain origin. We report a case of alveolar soft-part sarcoma arising in the right buccal mucosa in a 31-year-old woman.
The tumor measured 12×13×10mm. It was elastic soft and had ulceration on the surface. A granularcell tumor was suspected on examination of a biopsy specimen. The tumor was removed with the surrounding tissues. Histologically, the tumor consisted of large cells with eosinphilic cytoplasm. The cells showed distinct atypia and a nest-like arrangement.
PAS-positive diastase-resistant needle crystals were seen in the cytoplasm. Alveolar soft-part sarcoma was the final diagnosis. There has been no evidence of local recurrence or distant metastasis as of 1 year 6 months after operation.
