Abstract
A case of 42 year old female of pulmonary hamartoangiomyomatosis surgically verified, is reported. The following clinical aspects of interest were observed: normal results of spirometry and other clinical tests, hemoptysis and pneumothorax, related with menstruation. The former evidence may suggest that pulmonary obstructive disturbance which has been emphasized in previous reports, are not prerequisite for this diseased condition, and the latter, that the disease may be etiologically related to changes of female hormone, although this remains to be fully elucidated.