Abstract
A 63 year old man was admitted to our institute with a chief complaint of “Dyspnea”. The cardiopulmonary function tests revealed restrictive ventilatory disturbance and prominent alveolar hypoventilation with pulmonary hypertension.
The main causes of “dyspnea” were considered to be due to the intercostal muscle atrophy and weakness associated with fasciculations as a result of diaphragmatic kymography and biopsy of intercostal muscle findings.
He had no characteristic symptoms of amyotrophic lateral sclerosis, except slight atrophy of the small muscles of the hands in the early stage.
A rare case of amyotrophic lateral sclerosis was later diagnosed, by electromyogram and exaggeration of jaw reflex.
