2017 Volume 37 Issue 2 Pages 168-171
We report a case of anesthetic management of tympanoplasty in an infant with Waardenburg Syndrome（WS）. WS is an autosomal dominant inherited disease that is characterized by congenital sensorineural hearing loss, hair hypopigmentation, and pigmentary disturbances of iris. Less than 5 anesthetic experiences have been reported to date. Anesthetic considerations of WS are hearing loss, convulsion, muscle tone abnormality, and malnutrition. Our 20 month-old patient was scheduled for cochlear implantation with general anesthesia. Induction of general anesthesia was performed with nitrous oxide, oxygen, and sevoflurane. Air, oxygen, and sevoflurane were used for maintenance of anesthesia. Endotracheal intubation was uneventually performed using rocuronium 1 mg/kg. Pentazocine 3 mg was given as postoperative analgesia. Emergence from anesthesia was smooth. Postanesthetic course was also uneventful.
