Abstract
Fibrous dysplasia (FD) is a benign bone disease, and its cause is unknown. It is common on long bones and ribs, but rare in the head and neck region. FD frequently occurs in the maxilla and mandible, but rarely in temporal bone. The most common clinical manifestations of FD of temporal bone are hearing loss caused by stenosis of the external auditory canal, and ear canal cholesteatoma. Surgical treatment is the only treatment. However, restenosis of the external auditory meatus may occur after surgery, and there is no consensus on the surgical method or the timing of surgery. We report the case of an 11-year-old patient who underwent surgery and treatment because of hearing loss due to external auditory canal stenosis, and who experienced a good course.