In a 25-year period from 1954-1979, there were 53 cases of choledochal cyst operated on at the Tokyo University Hospital. Of those cases, 47 patients underwent pathological examination and hepatocholangiography, and were classified into six types Type I : Cystic dilatation of extra-hepatic duct with normal intrahepatic duct 12 cases ; Type II : Cystic dilatation both of extra and intra-hepatic ducts 10 cases ; Type III : Cystic dilatation of extrahepatic duct with fusiform intrahepatic duct 3 cases ; Type IV : Fusiform dilatation of extrahepatic duct with normal intrahepatic duct 1 cases ; Type V : Fusiform dilatation of extrahepatic duct with cystic intrahepatic duct none : Type VI : Fusiform dilatation both of extra-and intra-hepatic ducts 4 cases and Miscellany : Cystic dilatation of extrahepatic duct with unclarified intrahepatic ducts 17 cases. Anomalous arangement of the pancreaticobiliary ductal system was seen in 19 cases including 6 with elevated amylase level of the cystic content. Biopsy specimen of the liver showed marked fibrosis in 13 cases.