We exterienced a case of undifferentiated (embryonal) sarcoma of the liver which is rarely seen in children in Japan. An 8-year-old girl, was surgically treated for a large abdominal mass occupying the dome of the liver and bulging up the diaphragm. The tumor in the liver was removed by extended right hepatic lobectomy. Ten months later, however, the tumor recurred and she died. This paper presented the clinical course and pathohistological findings of undifferentiated (embryonal) sarcoma of the liver seen in our patient, which Stocker and Isak had described.