This is a case report of the essential fatty acid deficiency caused bv ED-AC. Three patients of Hirschsprung's disease with a short aganglionic segment were initially treated by ED-AC. All patients progressed well and did not require creation of a colostomy. Definitive operation (Duhamel's procedure) was performed when the body weight reached 5kg. Sparse hair was seen in one of the patients after ED-AC feeding for 2 months. Deficiency of essential fatty acids was thought to be the cause of sparse hair. The patient was then treated with Intralipid, which contains necessary fatty acids. Satisfactory hair growth was seen after the Intralipid treatment. For deficiency of essential fatty acids, it is important to use Intralipid while the patient is managed by ED-AC.
