Side-to-side duodenojejunostomy had commonly been used for congenital intrinsic duodenal obstruction such as annular pancreas and membranous stenosis in newborn period until a diamond-shaped duodenoduodenostomy was developed. Blind loop syndrome rarely occurs, but is an abominable complication after shunt operations of intestinal surgery. A girl, 13 years of age, with blind loop syndrome developing after duodenojejunostomy in the newborn period is reported. She complained of right upper abdominal pain, restriction of daily diet and weight loss for recent 2 years. After resecting a membranous (windsock web) of the duodenum and double duodenojejunostomy revealed by laparotomy, an end-to-back dudenojejunostomy has been performed to get a physiological pathway with favorable results. Long term follow-up study seems to be essential to patients who underwent duodnojejunostomy for congenital duodenal obstruction in newborn period.
