An 8-year-old girl with dermatomyositis was reffered because of right ureteral perforation. Initially, a tube nephrostomy was performed, but resulted in loss of the long segment ureter. After the complete clinical improvement of dermatomyositis, she was operated to provide internal contuinity of the right ureter. The vermiform appendix was utilized as a conduit from the right renal pelvis to the lower ureter with satisfactory function after one year and 6 months. Our satisfactory experience with one patient may show the efficacy of the appendix ureter-oplasty when the kidney has little mobility and the appendix has the required caliber and length.