Fibrous hamartoma of infancy (FHI) is a rare fibro-proliferating lesion arising from the subcutaneous tissue during the first 2 years of life. A case of fibrous hamartoma located in the right shoulder of an 11-month-old girl is reported. A firm, non tender, 2.5 × 2.2 × 1.0cm mass overlying the trapezius was excised. The histological diagnosis was FHI. Thirty one cases of FHI in Japanese literatures are reviewed. The mean age at operation was 13.9 months. Twenty four of 32 cases were male. The common sites of lesions were the axillae (7 cases), upper limbs (6), and lower limbs (6). The tumor was excised in 29 of 32 cases, and recurrence was reported only in a case. In 3 cases of partial resection, the remaining tumor showed no evidence of regrowth. These reports suggest that complete local excision is required as adequate therapy.