2025 Volume 61 Issue 4 Pages 728-733
In this article, we present a case of giant lymphatic malformation of the liver, which was successfully resected with no recurrence. A boy aged 1 year and three months presented with a complaint of abdominal distension. A diagnosis of abdominal lymphatic malformation was made on the basis of magnetic resonance imaging and ultrasonography findings. Three weeks later, he was admitted with progressive abdominal distension and vomiting, which caused respiratory failure. Ultrasound-guided drainage was performed in the intensive care unit, resulting in an improvement in his condition, and he was discharged in a week. However, he was readmitted three days after discharge owing to the recurrence of symptoms, which indicated the necessity of more advanced treatment. During laparotomy, we resected the mass arising from the visceral surface of the left lobe of the liver, extending into the abdominal cavity. The histopathological diagnosis was hepatic lymphatic malformation. Currently, he is symptom-free with no evidence of recurrence. Lymphatic malformation of the liver is rare. Although guidelines do not specify a certain strategy, this case suggests that surgical resection is effective for the lymphatic malformation of the liver.
