The Japanese Journal of Urology
Online ISSN : 1884-7110
Print ISSN : 0021-5287
ISSN-L : 0021-5287
BILATERAL PHEOCHROMOCYTOMAS AND ASYNCHRONOUS BILATERAL RENAL CELL CARCINOMAS ASSOCIATED WITH VON HIPPEL-LINDAU DISEASE: A CASE REPORT
Kazuya SuzukiEtsuko KosegawaTatsuhiko HoshiiNorio MiyajimaEisuke TakahashiRyusuke WatanabeKenji ObaraYoshihiko TomitaKohta TakahashiMinoru YoshidaMasahiro Yao
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2002 Volume 93 Issue 6 Pages 710-714

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Abstract
A 38-year-old man who had been followed with diagnosis of dilated cardiomyopathy and retinal angioma was referred to our hospital because of incidentally detected bilateral adrenal masses. Although he was normotensive, levels of catecholamine in urine were elevated and I131-MIBG scintigraphy showed accumulation in bilateral adrenal glands. Screening of central nervous system by MRI revealed cerebellar hemangioblastoma. Right adrenalectomy and left partial adrenalectomy were performed, both of which tumors pathologically diagnosed as pheochromocytoma, followed by resection of the cerebellar hemangioblastoma. Five months later, abdominal CT revealed a left renal tumor and underwent left partial nephrectomy, being diagnosed as renal cell carcinoma. A right renal tumor was detected on follow up CT at 1 year after the partial nephrectomy. Since cardiac function was deteriorated, we have followed with careful observation. This is the second documented case of bilateral renal cell carcinomas and bilateral pheochromocytomas with VHL in Japan.
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