結節性硬化症に合併した腎細胞癌の1例

齋藤 満; 柿沼 秀秋; 飯沼 昌宏; 土谷 順彦; 下田 直威; 大山 力; 佐藤 滋; 佐藤 一成; 加藤 哲郎

doi:10.5980/jpnjurol1989.94.634

A CASE OF RENAL CELL CARCINOMA IN TUBEROUS SCLEROSIS

Mitsuru Saito, Hideaki Kakinuma, Masahiro Iinuma, Norihiko Tsuchiya, Naotake Shimoda, Chikara Ohyama, Shigeru Satoh, Kazunari Sato, Tetsuro Kato

Author information

Mitsuru Saito
Department of Urology, Akita University School of Medicine
Hideaki Kakinuma
Department of Urology, Akita University School of Medicine
Masahiro Iinuma
Department of Urology, Akita University School of Medicine
Norihiko Tsuchiya
Department of Urology, Akita University School of Medicine
Naotake Shimoda
Department of Urology, Akita University School of Medicine
Chikara Ohyama
Department of Urology, Akita University School of Medicine
Shigeru Satoh
Department of Urology, Akita University School of Medicine
Kazunari Sato
Department of Urology, Akita University School of Medicine
Tetsuro Kato
Department of Urology, Akita University School of Medicine

Keywords: renal cell carcinoma, tuberous sclerosis

JOURNAL FREE ACCESS

2003 Volume 94 Issue 6 Pages 634-638

DOI https://doi.org/10.5980/jpnjurol1989.94.634

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Abstract

A 43-year-old woman with mental retardation, epilepsy, and urinary stone disease had a right renal tumor. Acne-like anthema around the nose and dental pits of the nine teeth were typical signs of tuberous sclerosis (TSC), and the biopsy finding of the facial anthema was consistant with TSC. The pathological diagnosis of laparoscopic nephrectomy was renal cell carcinoma in the hemorrhagic cyst. The TSC-related renal cell carcinoma tends to develop bilaterally in younger individuals compared with the sporadic RCC. This case is the 27th case of TSC-related RCC in Japan.

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