Abstract
A 30-year-old man had a thumb-size nodule on the extensor surface of right articulatio pedis. Four years after the excision, the tumor recurred at the same area and amputation of rt. lower leg was performed. Twelve years later, metastases to the scalp and lung were evident. Wide excision of the scalp tumor was done and adjuvant chemotherapy prescribed. He is living. Histopathologically, the tumor consisted of atypical fibroblast-like cells, atypical epithelioid cells, proliferated fibrous connective tissue and central necrosis. An electron microscopic examination revealed numerous well-developed rER in fibroblast-like cells and filopodia in the epithelioid cells.