Abstract
A 1-month-old girl presented with multiple confluent plaques of varying sizes that were slightly raised from the skin surface on the mid-back to the right side and had been present since birth. The plaques were generally pale-yellow in color with a granular surface. Histopathologically, the lesions showed immature hair follicles with mild papillomatosis and hyperplasia of the sebaceous glands, and organoid nevus was diagnosed. The distribution pattern appeared to be type III (phylloid pattern) of Happle's mosaic distribution pattern. At present, no other abnormalities besides skin symptoms have been observed, for example, in the central nervous system and skeletal system. However, keeping sebaceous nevus syndrome in mind, careful observation should be considered due to the pathognomonic distribution of plaques.
