Patients with spina bifida often have hip dislocation. We report a case of unilateral hip subluxation with spina bifida. A 16-year-old girl suffered left hip pain when walking. We performed operative treatment in two phases; first, we performed arthrodiatasis on the left hip. After about five weeks, the femoral head moved about 3cm, and was positioned on the same level as the other femoral head. In the second phase we performed Chiari osteotomy, varus derotational osteotomy, and transfer of the external oblique muscle. After two weeks postoperativle, she was able to move around using a wheel chair. She is now able to walk without crutches or hip pain. It is often difficult to perform acetabuloplasty for dislocation or subluxation of the hip with spina bifida. However, if arthrodiatasis is first performed, acetabuloplasty may also be considered for hip dislocation or subluxation.