In this study, we report a very rare case of malignant peripheral nerve sheath tumor (MPNST) arising in the finger tip. A 78 -year-old woman complained of right ring-finger pain and soft tissue mass. We underwent open biopsy of the tumor, and found that the tumor had spread toward the proximal along the digital nerve. The case was diagnosed as MPNST in addition to the histological results. Because of the malignancy, wide excision was performed including ring-finger amputation from the base of the fourth metacarpal bone. No recurrence and metastasis were found for eleven months after surgery. To our knowledge, malignant tumor in the finger is very rare, and no case of MPNST arising in the finger has been reported.
