A case of Chondromyxoid fibroma was reported. The patient was a 4-year-old boy, and the proximal metaphysis of the right femur was affected. Curretage and Kiel bone graft was performed in the lesion, but 4 months after the first operation, he had a local recurrence. In 1948 Jaffe and Lichtenstein reported a series of bone tumors as chondromyxoid fibroma, emphasizing that this newly recognized entity was likely to be mistaken for chondrosarcoma but was a benign growth. Chondromyxoid fibroma of bone was a rare and benign tumor. Especially, there had been few reports of the tumor under 4 years old. We should carefully follow up this case, because several cases of malignant change from this tumor were reported.
