A 15-year-old boy with known recessive dystrophic epidermolysis bullosa was admitted to our hospital for surgery to his mitten hand. The thumb was contracted in adduction, and all other four fingers were fused with flexion contracture of the MP joint. Bilateral fingers were freed surgically with open method, and only the right hand was immobilized with a special apparatus in the early post-operative period. But flexion deformity of DIP joint at left middle and ring finger could not be freed because of its capsular and ligamentous contracture.
