2008 Volume 67 Issue 4 Pages 242-245
A 32-year-old man who suffered from abdominal pain and vomiting was referred to our hospital urgently. He had been diagnosed with Peutz-Jeghers syndrome (PJS) in his childhood, and has undergone partial resection of small intestine due to intussusception at 13 years old. He was diagnosed with intussusception by abdominal computed tomography that showed the target sign in the right side abdomen. An emergency operation was performed because of the diagnosis of ileus due to intussucseption. Operative findings revealed intussusception of the small intestinal type. Manipulation of the intestinal invagination and partial resection of the necrotic intestine were undergone. A pedunculated polyp was found in the apical portion of the intestine, and three other polyps were found in the jejunum. The pathological findings revealed hamartomatous polyps of PJS type. It is possible that the recurrence of intussusception, malignant alteration of polyps, and malignant tumor except for alimentary tract can occur in PJS. Therefore it considered that long-term follow up is important for patients with PJS.
