Pediatric Dental Journal
Online ISSN : 1880-3997
Print ISSN : 0917-2394
ISSN-L : 0917-2394
Case Report
Dental management of 49,XXXXY syndrome with taurodontism: A case report
Hiroe KodairaKohachiro OhnoMasamichi IdeShiki AdachiYoshinobu Asada
Author information

2009 Volume 19 Issue 2 Pages 262-266


A Japanese male with a karyotype of 49,XXXXY was presented for dental treatments from 6 years to 20 years of age. The patient had pulmonary stenosis as well as mental retardation, hypogonadism, fifth finger and toe clinodactyly, genu valgus, pes cavus and mandibular prognathism. Dental manifestations revealed multiple caries and taurodontism of both primary and permanent dentitions and hypodontia in permanent dentition. Dental management of a patient with 49,XXXXY syndrome is important to accomplish both controlling behavioral problems and medical considerations for preventing infective endocarditis.

Information related to the author

This article cannot obtain the latest cited-by information.

© 2009 by The Japanese Society of Pediatric Dentistry
Previous article Next article