Recent experience with 2 cases of congenital biliary dilatation which manifested with delivery as a turning point is described. In addition such cases with clinical manifestations coming from pregnancy or delivery were reviewed in the Japanese literature and their clinical pictures were statistically analyzed.
Case 1 was a 30-year-old primipara. Pancreatitis-like symptoms appeared from the day 12th after delivery. As a result of close examination, the patient was diagnosed as congenital biliary dilatation with anomalous arrangement of bile duct confluence (Ic(p)). Case 2 was a 27-year-old primipara. She complained of abdominal pain on the 9th day after delivery. From minute examinations she was diagnosed as congenital biliary dilatation of Ic(p) IIcm. In both cases cystectomy and hepatojejunal Roux-en Y anastomosis were performed.
In the past three decades (1961-1990), 77 cases have been reported in Japan. Of the 77 cases, 66 cases developed clinical symptoms during pregnancy, 7 did after delivery, and 4 of unknown. These cases predominantly had cystic dilatation. This disease most commonly manifested during 3 months from 6th to 8th month of pregnancy.