家族性難聴の小児における問題点

抄録

When hearing impaired children acquire their mother tongue, early diagnosis and early speech training are important.
If their parents were deaf, their children's audiological background would be poor compaired with than that of deaf children whose parents were not deaf.
We reported the problems on the diagnosis and on the acquirement of their mother tongue in those children.
In twenty-two children with hereditary deafness only three children visited doctors, because they had deaf persons in their family. In the fourteen children hearing impairments were pointed out in pre-school or in school at audiological examination as a routine.
The problems on the diagnosis and on the acquirement of their mother tongue were as follows.
1. Hearing impaired parents can not catch their children's speech fully.
2. They can not cacth their children's reaction to the sounds.
3. They can not catch the level of language development of their children.
4. They take no notice of their children's poor pronunciation.
5. They can not cacth the change when their children's impairment becomes worse.