頭蓋顔面正中低形成に伴う呼吸障害症例

抄録

Children with Cranio-facial anomalies frequently show upper airway obstruction with a wide variety of symptoms, ranging clinically from mild nasal obstruction to severe respiratory distress. Case 1 was a 2 m/o boy with Hallermann-Streiff syndrome who had developed and suffered from feeding difficulty and obstructive sleep apnea for a month. Endoscopic findings showed bilateral nasal stenosis and macroglossia with mandibular dysostosis caused his respiratory dysfunction. Case 2 was a 3 m/o girl with Crouzon syndrome. We found nasal cavity and nasopharyngeal stenosis due to midface retrusion synchronized with respiration.
Stenting technique on nasopharyngeal airway relieved the respiratory embarrassment in both cases.