We report a unique case of bleeding lumbar myxopapillary ependymoma, causing superficial siderosis (SS), which is characterized by the deposition of hemosiderin in the leptomeninges on the surface of the brain, cranial nerves, and spinal cord. A 67-year-old man, presenting with progressive hearing disturbance and ataxia, was diagnosed with SS by brain MRI. The source of hemorrhage was a cauda equina ependymoma, which was surgically removed. Early identification of the hemorrhage source is important in the treatment of SS, and neurosurgical intervention to the causal lesion can prevent neurological deterioration.
