The dichotic listening performance in children was examined. The digits were used for investigating dichotic listening performance in children. The digits were presented through earphones on both ears simultaneously in 60 right-handed normal children aged 5 to 10 years. Stimulus durations were 700 msec for each digit. Right ear advantage was observed for subjects between 5 to 7 years old. Reactions misheard the one ear stimuli to the other ear each other and answered correctly two stimuli to the both ears were found significantly more frequently in the 7-years-old group than others respectively.
When hearing impaired children acquire their mother tongue, early diagnosis and early speech training are important. If their parents were deaf, their children's audiological background would be poor compaired with than that of deaf children whose parents were not deaf. We reported the problems on the diagnosis and on the acquirement of their mother tongue in those children. In twenty-two children with hereditary deafness only three children visited doctors, because they had deaf persons in their family. In the fourteen children hearing impairments were pointed out in pre-school or in school at audiological examination as a routine. The problems on the diagnosis and on the acquirement of their mother tongue were as follows. 1. Hearing impaired parents can not catch their children's speech fully. 2. They can not cacth their children's reaction to the sounds. 3. They can not catch the level of language development of their children. 4. They take no notice of their children's poor pronunciation. 5. They can not cacth the change when their children's impairment becomes worse.
We report a case of Landau-Kleffner syndrome with bilateral moderate peripheral hearing loss. Her hearing loss became apparent at age of 3. ABR showed 40∼45 dB threshold elevation. She was given hearing aid fitting and auditory training. At age of 5 years, suddenly she did neither respond to speech sounds nor speak words. She could recognize environmental sounds, but neither verbal stimulus nor melodies. EEG showed bilateral difused spike and wave complex. Though anticonvulsants were prescribed for her, her signs continued and she entered a school for deafness. At age of 7 years she gradually began to speak words again. Now she is 13 years old. Both central hearing disorders and inner speech disorders still continue. Auditory comprehension is severely impaired and so she has severe language retardation. We consider that her language disorders would be caused by both peripheral hearing loss and the central auditory and inner speech disorders.
The factors causing delay on speech and language development were statistically studied. Subjects were 380 children who were diagnosed as “delayed speech and language development” at our clinic from 1977 to 1990. None of these children had moderate or severe hearing loss. First, possible causal factors were pointed out. Then subjects were devided into groups according to the factors. Finally the capability of daily conversation at one's last interview was judged by using four step scale. The relations between each factor group and daily conversation ability were discussed. The findings were as follows: 1. Mental deficiency was seen in 43% of the subjects. The capability of daily conversation varied among children with mental deficiency. 2. A group of young children who had no or little speech but did not have any apparent causal factors became capable of having daily conversation. 3. Children whose IQ were between 75 to 90 and/or who showed fine motor disfunction also became capable of having daily conversation.
The language development of two infants with organic brain disorders who stayed at a sucklinghospital, and language development of 50 children in the same hospital, were reported. The first boy showed so-called battered child symdrome. When he was one month old, he wasfound to have cranial bones fracture, contusion of the brain, and cerebral hemorrhage. The brainCT scan revealed a lesion including Broca and Wernicke areas, and his physical and communicativedevelopment on the whole was delayed. After he was gave communicative counselins with his caretakers, and better bringing up, his language DQ improved from 69.2 to 87.5. The second boy hadmild hearing loss, and autistic tendencies. When his mother was 13 years old, he was born after anincestual relationship. He developed neither language nor social interaction. After counseling insocial and hearing skills, his language DQ improved from 50 to 87.5. The average language DQ of 50 children in the same hospital at the time of leaving became better than at entering. Languagedevelopment was still delayed.
nchial anomalies, hearing loss and renal dysplasia, being regarded as an autosomal dominant disorder. We presented an 8-year-old girl who had bilateral preauricular pits, bilateral lateral cervical fistulae, and mixed type of bilateral hearing loss. The cause of hearing loss was determined as ossicular deformity and cochlear hypoplasia using CT films. Renal dysplasia was not detected. She underwent surgery for the branchial anomalies with uneventful course. Her father also had branchial anomalies.
We have reported two patients with Kabuki make-up syndrome who exhibited mild sensorineural hearing loss. It has been reported that the hearing loss in cases of Kabuki makeup syndrome is conductive and caused by otitis media. The hearing loss in our own cases was suspected of being sensorineural and congenital, because the patients had no history of labyrinthitis or meningitis which acttected the inner ear. We suggest in the Kabuki makeup syndrome, congenital sensorineural hearing loss might be present and that the pathogenesis ofthis hearing loss might be caused by abnormal embryogenesis.