The patient was a 30-year-old man who had become aware of a mass in his left cheek around the age of 17. He consulted our department after noticing that the mass was gradually increasing in size. We noted a fist-sized mass with limited mobility in the anterior portion of the left ear and following various examinations, we suspected a primary malignant tumor of the accessory parotid gland. No apparent lymph node metastasis or distant metastasis was observed, and surgery involved left parotidectomy, resection of the skin and parotid gland, and left neck dissection. Thereafter, we reconstructed the buccal branch of the facial nerve with the great auricular nerve and closed the skin defect with a rotation-advancement flap. A postoperative pathological examination led to a diagnosis of mammary analogue secretory carcinoma with sarcomatoid change.
The patient underwent subsequent chemoradiotherapy, but experienced recurrence and repeat metastasis and died 15 months postoperatively.