2022 Volume 65 Issue 1 Pages 60-65
Paget's disease causes progressive sensorineural or mixed hearing loss. However, reports of cochlear implantation for hearing loss in patients with Paget's disease is rare. We encountered a case of Paget's disease of the bone with severe hearing loss in whom we performed cochlear implant surgery. The patient was a 66-year-old man who had suffered from bilateral progressive sen
sorineural hearing loss from the age of 50 years. We performed right cochlear implantation, without any surgical complications. The result in the post-operative word recognition test (CI2004) was 80%. The outcome of the cochlear implant surgery was good, even though preoperative high resolution CT showed bilateral internal auditory canal stenosis; this might suggest that stenosis of the internal auditory canal might not necessarily indicate cochlear nerve dysfunction in patients with Paget's disease. Since drug therapy for Paget's disease can prevent the progression of hearing impairment, but has no effect on hearing impairment that has already developed, patients with Paget's disease presenting with severe sensorineural hearing loss could be good candidates for cochlear implantation.
