Abstract
1) The unilateral deafness was found in 12.1% of all the patients of sensori-neural deafness.
2) There were several audiometric patterns such as gradual sloping form, flat form, rising form and dip form.
3) The total deafness mostly occurred in childhood, and the other types of deafness occurred in young adults, the fourth and fifth decades of age.
4) By recruitment test, Békésy audiometer, speech audiometer, speech audiometer, tone decay test and electrocochleography, the lesions were estimated as peripheral in most of the cases, but the retrolabyrinthine type was also encountered.
5) With a long-term follow-up for more than 2 years, progressive sensori-neural hearing loss and fluctuating sensori-neural hearing loss were found.
6) HLA was examined and HLA-AW33 was slightly dominant.