Congenital Cystic Adenomatoid Malformation of the Lung: Report of a Successful Surgical Case

Abstract

A case of congenital cystic adenomatoid malformation of the lung (CCAM) is reported. A 9-day-old newborn infant underwent successful lobectomy for CCAM. The lesion in the resected left lower lobe was composed of multiple large cysts. The cysts were lined by ciliated pseudostratified columnar epithelium with numerous polypoid projections. The wall of the cysts contained prominent smooth muscle and elastic tissue. Mucus producing cells were also present, however cartilage was not seen in the wall. Smaller cysts resembled dilated respiratory bronchioles or large alveoli were present adjacent to the larger cysts.