A Case of Neutrophilic Urticarial Dermatosis, Associated with Anti-ARS Antibody-positive Amyopathic Dermatomyositis

Abstract

We report a case of neutrophilic urticarial dermatosis, associated with amyopathic dermatomyositis. The female patient presented with urticarial erythema, which histopathologically showed a dense dermal neutrophilic infiltrate with no signs of leukocytoclastic vasculitis. In addition, there was a neutrophilic infiltrate within the eccrine gland, a unique histopathological finding. Dermatologists should be aware of this new entity, because it may be associated with various auto-immune or auto-inflammatory diseases.