1995 Volume 37 Issue 10 Pages 2257-2261_1
Acase of idiopathic portal hypertension accompanied by periosis hepatis was reported. A13-year-old man vvas admitted to our hospital because of further evaluation of liverdysfunction and splenomegaly. Hematology showed mild thrombocytepenia. Abdominal US, CT, MRI showed splenomegaly and dilatation of portal, superior mesenteric andsplenic veins. Histology of the liver showed a dilatation of portal vein in the portal area, proliferation of collagen fibers, and than septal fibrosis. In addition, various forms of bloodfilled cavities within the hepatic parenchyma suggesting perioSis hepatis were demonstrated. With these histological findings, a peculiar appearance consisting of mildly granularliver surface accompanied by dark, royal purple speckles(spats)was demonstrated by Iaparoscopy.
