Abstract
Three cases of duodenal gangliocytic paraganglioma experienced during last 10 years at our hospital were evaluated from the clinical aspect with addtional review of the literature. This neurogenic tumor is extremely rare. However, it arises from the second portin of the duodenum, especially in the vicinity of the papilla of Vater in the majority of cases. A peticular shape consisted of uneven and nodular submucosal tumor with erosion and ulcer on the surface make the diagnosis of this tumor easy. This tumor should be surgically operated in the earlier stage from the viewpoints of accompanying bleeding from the tumor, pancreatitis, obstructive jaundice and regional lymph nodes metastasis in some cases.