Abstract
A 32-year-old woman was admitted to our hospital with high temperature and diarrhea. She was previously diagnosed with intestinal Behcet's disease after perforation of an ileocecal ulcer 4 years prior, and at that tame, she did not have pneumatosis cystoides intestinalis. Plain x-ray film of the abdomen showed lineal gas in the wall of the ascending colon. Colpnpscopy revealed multiple submucosal tumor-like, smooth and elastic-soft hemispherical elevated lesions as well as multiple small ulcers in the ascending colon. We diagnosed this case as pneumatosis cystoides intestinalis (PCI) of the ascending colon associated with intestinal Behcet's disease. Upon treatment of Behcet's disease with salazopirine, abdominal symptoms improved and radiographic findings also disappeared, suggesting a relationship between intestinal Behcet's disease and PCI. We present here the first case of PCI associated with Behcet's disease.